Dental prosthetic rehabilitation of a child with ectodermal dysplasia: A case report
نویسندگان
چکیده
Ectodermal dysplasias (EDs) form a part of the complex group of rare congenital diseases, primarily observed as a result of the abnormal development of embryonic ectodermal derivatives. A 5-year-old male child reported to the Department of Pedodontics and Preventive Dentistry, with the typical features of hypohidrotic ectodermal dysplasia (HED), i.e., diff usely sparse hair, eyelashes and eyebrows, subsequent problems with thermoregulation and dry skin. The facial profi le showed a prominent forehead, sunken nasal bridge (“saddle nose”), and everted lips. Oral prosthetic rehabilitation was planned for the child to improve both the vertical and sagittal skeletal relationship, additionally providing better esthetics, improved speech, and masticatory function. The case report thus presents the early prosthetic oral rehabilitation of a young boy with HED associated with severe anodontia in the primary dentition.
منابع مشابه
Oral Rehabilitation of Hypohidrotic Ectodermal Dysplasia – A Case Report and Review
Ectodermal dysplasia is a hereditary disorder that occurs due to consequence of disturbances in the ectoderm of the developing embryo. It is usually accompanied by lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. A case report illustrating the prosthetic rehabilitation by flexible and removable partial denture for a girl child of 9 years with Ectoder...
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Alveolar ridge is underdeveloped in ectodermal dysplasia (ED). The available treatment plans include fixed, removable or implant-supported prostheses, alone or in combination. A 5 year-old boy was referred for treatment to the Department of Prosthodontics, Tehran University of Medical Sciences with the chief complaint of missing teeth. Prosthodontic treatment was performed to improve masticatio...
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Ectodermal dysplasia (ED) is a genetically heterogeneous condition resulting from clinical anomalies of structures derived from the ectoderm, such as the hair, nails, sweat glands, and teeth. This clinical report presents the case of a child diagnosed with hypohidrotic ED at 2 years of age; clinical and imaging evaluation was performed with 6-year follow-up, and we present details of the prosth...
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